ISSN:
1432-0533
Keywords:
Bielschowsky bodies
;
Lafora body
;
Status marmoratus
;
Polyglucosan
;
Anoxic encephalopathy
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Summary Intraneuronal inclusions, consisting of polyglucosan and having histochemical and ultrastructural features identical to Lafora body of familial myoclonic epilepsy (Unverrict-Lafora disease), have been found restricted to the lateral pallidum in five patients. Two of these patients were also found to have status marmoratus of the basal ganglia. These lateral pallidal inclusions have been named after Bielschowsky, their original discoverer. We report two additional patients with status marmoratus and Bielschowsky bodies and suggest that these two conditions are frequent concomitant phenomena arising independently from a common cause.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF00691185
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