ISSN:
1432-1076
Keywords:
Letterer-Siwe disease
;
Protein losing enteropathy
;
Immunodeficiency
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Abstract A case of congenital Letterer-Siwe disease associated with protein losing enteropathy is presented. The patient was born at term after an uneventful pregnancy, and generalized eczematous skin eruptions were observed at birth. Excessive protein loss from the intestine was recognized. A cutaneous biopsy from typical lesions revealed histiocytic infiltrations and Langerhans' cell granules in the cytoplasm of the histiocytes.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF00445898
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