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  • 1
    Electronic Resource
    Electronic Resource
    An unusual late-onset case of propionic acidaemia: biochemical investigations, neuroradiological findings and mutation analysis (1997)
    Springer
    European journal of pediatrics 157 (1997), S. 50-52 
    Details
    ISSN: 1432-1076
    Keywords: Key words Propionic acidaemia ; Basal ganglia ; PCC gene mutations
    Source: Springer Online Journal Archives 1860-2000
    Topics: Medicine
    Notes: Abstract We report a 5-year-old boy with propionic acidaemia who developed a rapidly fatal necrosis of the basal ganglia after an episode of clinical deterioration. Neither metabolic acidosis nor hyperammonaemia were present. Organic acid analysis in both urine and CSF showed increased levels of methylcitric and 3-hydroxypropionic acids. Propionic acidaemia was confirmed by demonstrating a propionyl-CoA carboxylase deficiency (11% of control value) in skin fibroblasts. DNA analysis revealed that the patient was a compound heterozygote for two mutations in the PCCB gene. Conclusion Propionic acidaemia can present as a sudden and fatal neurological disease and not only as an organic aciduria with severe biochemical dis-turbances and progressive neurological deterioration.
    Type of Medium: Electronic Resource
    URL: http://dx.doi.org/10.1007/s004310050765
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  • 2
    Electronic Resource
    Electronic Resource
    On serializability (1985)
    Springer
    International journal of parallel programming 14 (1985), S. 387-403 
    Details
    ISSN: 1573-7640
    Keywords: Database ; transaction ; concurrency ; serializability ; families of schedules
    Source: Springer Online Journal Archives 1860-2000
    Topics: Computer Science
    Notes: Abstract Concurrent execution of database transactions is desirable from the point of view of speed, but may introduce inconsistencies. A commonly used criterion of correctness of a concurrent execution of transactions is serializability, i.e., the equivalence of the execution to some serial schedule or schedules. In the literature several transaction models have been used and several different notions of serializability have been introduced. In this paper, we investigate the various serializability families in the general transaction model, in the two-step model, and in the restricted two-step model. We also examine these families in the multiversion database model.
    Type of Medium: Electronic Resource
    URL: http://dx.doi.org/10.1007/BF00991181
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    Paper (German National Licenses)
    Fulltext
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