ISSN:
1432-0533
Keywords:
Spinocerebellar atrophy
;
Dementia
;
Plaques
;
Slow virus
;
Spongiform encephalopathies
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Summary Report of two unrelated cases of a rare familiar disease of degenerative nature, from a clinical point of view belonging to the spinocerebellar atrophies, combined with dementia. According to the pedigrees, the disease can be followed up to 3–4 generations. Microscopic study reveals glioneuronal dystrophy with spongiform changes together with kuru plaques and atypical plaque-like formations, hitherto only described in this disease. Nosological aspects of these findings are discussed.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF00707108
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