ISSN:
1433-0350
Keywords:
Key words Atypical teratoid tumor
;
Children
;
Extrarenal rhabdoid tumor
;
Medulloblastoma
;
Primitive neuroectodermal tumor
;
Rhabdoid tumor of the CNS
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Abstract Malignant rhabdoid tumor (MRT) is a recently described variety of childhood renal neoplasm. MRT arising primarily in the central nervous system (CNS) is still a rather unfamiliar pathological entity and is frequently misdiagnosed as medulloblastoma or primitive neuroectodermal tumor (PNET). We describe a 7-month-old boy who harbored a CNS-MRT that originated within the IV ventricle and invaded the brain stem and the cerebellar hemispheres. After an initial documented good response to chemotherapy the tumor recurred locally 9 months after operation. We discuss clinical and histopathological features distinguishing between PNET/medulloblastoma and MRTs. Current literature on MRT of the CNS is briefly reviewed.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/s003810050112
Permalink
