Library

feed icon rss

Your email was sent successfully. Check your inbox.

An error occurred while sending the email. Please try again.

Proceed reservation?

Export
  • 1
    Electronic Resource
    Electronic Resource
    Springer
    European journal of pediatrics 140 (1983), S. 5-12 
    ISSN: 1432-1076
    Keywords: Proteus syndrome ; Macrodactyly ; Hemihypertrophy ; Pigmented nevi ; Skull anomalies ; Lipomas
    Source: Springer Online Journal Archives 1860-2000
    Topics: Medicine
    Notes: Abstract Four boys are described with partial gigantism of the hands and/or feet, pigmented nevi, hemihypertrophy, subcutaneous hamartomatous tumors and macrocephaly, and/or other skull anomalies. Three of these patients showed an accelerated growth in their first years of life. Two suffered from cystiform pulmonary abnormalities. The children showed normal mental development with the exception of one with traumatic brain damage. Parental consanguinity was not disclosed. As a result of a review of the literature, we can say that these cases do not conform to any well defined entity and would appear to represent a ‘new’ syndrome to be categorized under congenital hamartomatous disorders. The mode of inheritance of the undoubtedly genetically determined syndrome is yet not clearly understood. We propose the term Proteus syndrome for this ‘new’ syndrome.
    Type of Medium: Electronic Resource
    Library Location Call Number Volume/Issue/Year Availability
    BibTip Others were also interested in ...
  • 2
    ISSN: 1435-1285
    Keywords: Key words Adult congenital heart disease — vena cava abnormalities — atrial switch operation — systemic venous obstruction — spiral computed tomography — 3-dimensional reconstruction ; Schlüsselwörter Angeborene Herzfehler — Hohlvenenanomalie — Vorhofumkehroperation — Hohlvenenobstruktionen
    Source: Springer Online Journal Archives 1860-2000
    Topics: Medicine
    Description / Table of Contents: Summary We report spiral-CT findings in adult patients with congenital abnormalities of the vena cava and systemic venous obstructions after atrial switch operation. Especially systemic venous obstruction is a well-known complication following Mustard procedure for transposition of the great arteries. The results demonstrate that computed tomography, particularly with the use of 3-dimensional surface reconstruction, is very useful as a highly sensitive procedure for the detailed depiction of abnormalities of the vena cava or of residua and sequelae after inflow correction for complete transposition. Demonstration of such abnormalities or obstructions after atrial switch operation is important, since the recognition and quantitation of caval anomalies by clinical techniques is unreliable and indeed often impossible. Imaging procedures such as spiral computed tomography are important for this purpose. Advantages of spiral computed tomography, particularly with 3-dimensional reconstructions, are discussed.
    Notes: Zusammenfassung Anomalien im Bereich der oberen Hohlvene kommen häufig vor. Sie können Krankheitswert haben, technische Probleme bei Untersuchungen oder Behandlungen verursachen und intra- oder postoperativ den Erfolg komplexer Operationen (z.B. Vorhofumkehr-, Fontan-OP) gefährden. Obstruktionen der Hohlvenen treten bei mehr als 10% der Patienten mit Vorhofumkehroperation bei kompletter Transposition der großen Arterien auf. Zur detaillierten Erfassung von angeborenen Anomalien und erworbenen Veränderungen der großen Venen ist die Computertomographie als hochsensitives Verfahren mittlerweile sehr gut geeignet. Die Spiralcomputertomographie ermöglicht es, bei geringer Invasität, ein Organvolumen wie den Thorax innerhalb einer Atemphase komplett computertomographisch zu erfassen. Multiplanare Sekundärschnitt-Rekonstruktionen liefern in beliebigen Ebenen detaillierte Informationen über Gefäßverläufe oder pathologische Prozesse. 3-D-Oberflächendarstellungen ergeben ohne zusätzliche Strahlenbelastung eindrucksvolle Bilder der Lagebeziehung intrathorakaler Gefäßstrukturen zueinander und eignen sich daher besonders gut, eine räumliche Vorstellung komplexer Gefäßsituationen zu erhalten.
    Type of Medium: Electronic Resource
    Library Location Call Number Volume/Issue/Year Availability
    BibTip Others were also interested in ...
  • 3
    Electronic Resource
    Electronic Resource
    Springer
    Langenbeck's archives of surgery 327 (1970), S. 1035-1038 
    ISSN: 1435-2451
    Source: Springer Online Journal Archives 1860-2000
    Topics: Medicine
    Type of Medium: Electronic Resource
    Library Location Call Number Volume/Issue/Year Availability
    BibTip Others were also interested in ...
  • 4
    Electronic Resource
    Electronic Resource
    Springer
    Langenbeck's archives of surgery 325 (1969), S. 672-675 
    ISSN: 1435-2451
    Source: Springer Online Journal Archives 1860-2000
    Topics: Medicine
    Description / Table of Contents: Zusammenfassung Im Zeitraum von 1958–1968 wurden 71 Patienten mit Anurie urologisch untersucht und behandelt; 41% der Kranken hatten anatomisch oder funktionell nur eine Niere. Häufigste Ursache der Anurie war bei Männern der ein- oder beidseitige Steinverschluß des Ureters, bei Frauen Harnleiterobstruktion bei gynäkologischen Tumoren. Die Therapie bestand aus instrumentellen (Ureterkatheter, Schlinge) und operativen (Lithotomie, Nephrostomie) Maßnahmen; in 13 Fällen mußte präoperativ dialysiert werden. Frühletalität 32%.
    Notes: Summary In the period 1958–1968, 71 patients with anuria have undergone urological examination and received treatment. 41% of the patients had only one kidney either anatomically or functionally. The most frequent cause of the anuria in males was either a unilateral or bilateral stone-occlusion of the ureter and in females ureteral occlusion because of gynaecological tumors. Therapy consisted of instrumental (ureteral catheter or loop) and operative (lithotomy or nephrostomy) measures. In 13 cases, pre-operative dialysis was necessary. Mortality 32%.
    Type of Medium: Electronic Resource
    Library Location Call Number Volume/Issue/Year Availability
    BibTip Others were also interested in ...
Close ⊗
This website uses cookies and the analysis tool Matomo. More information can be found here...