ISSN:
1432-1076
Keywords:
4-Hydroxyisovaleric acid
;
3-Methyl-γ-butyrolacetone
;
Isovaleric acidemia
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Abstract In addition to N-isovalerylglycin, isovaleric, 3-hydroxyisovaleric and methylsuccinic acids the excretion of previously unreported 4-hydroxyisovaleric acid in isovaleric acidemia is described. The new metabolite seems to be an intermediate product in the formation of methylsuccinic acid from isovaleric acid by omega-oxidation.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF00442995
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