Abstract
A case of congenital portalsystemic shunting due to an intrahepatic connection diagnosed by ultrasound scanning and color Doppler in an 8-month-old girl is reported. She began to manifest trimethylaminuria 3 years later. At 7 years of age, she is asymptomatic without therapeutic measures except for diet. This is the seventh reported case and the third in a child to our knowledge.
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Fernández, M.S., Gutiérrez, C., Vila, J.J. et al. Congenital intrahepatic portocaval shunt associated with trimethylaminuria. Pediatr Surg Int 12, 196–197 (1997). https://doi.org/10.1007/BF01350000
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DOI: https://doi.org/10.1007/BF01350000