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Crowned dens syndrome: a manifestation of hydroxy-apatite rheumatism

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Summary

Crowned dens syndrome is defined as an association of acute cervical pain and calcifications in the peri-odontoid space. The authors report one case of this rare localization of hydroxy-apatite rheumatism and review 12 similar cases in the literature. This disease affects only adult females. Patients present with inflammatory signs, can be treated with non-steroid anti-inflammatory drugs and recover without sequela. Calcium pyrophosphate dihydrate deposition can also lead to this syndrome. Other perioodontoid calcifications and ossifications, usually asymptomatic, appear only as a radiologically crowned dens.

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Authors and Affiliations

  1. Department of Neurosurgery, Hôpital Sainte Marguerite, Marseille, France

    S. A. Malca, P. H. Roche, W. Pellet & A. Combalbert

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  1. S. A. Malca
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  2. P. H. Roche
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  3. W. Pellet
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  4. A. Combalbert
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Malca, S.A., Roche, P.H., Pellet, W. et al. Crowned dens syndrome: a manifestation of hydroxy-apatite rheumatism. Acta neurochir 135, 126–130 (1995). https://doi.org/10.1007/BF02187755

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