Summary
A case of imflammatory myopathy with faciopharyngoproximal distribution is reported. It is very unusual for facial weakness to be a major feature in polymyositis, but when other muscles are involved the clinician should be stimulated to look for an inflammatory myopathy. Marked improvement may be achieved as a result of corticosteroid therapy.
Zusammenfassung
Wir berichten über einen Fall einer entzündlichen Myopathie mit fazio-pharyngo-proximaler Beteiligung. Fazialisparese als wichtigstes Zeichen ist ungewöhnlich im Rahmen einer Polymyositis. Die besondere Verteilung der Muskelschwäche, welche unsere Patientin aufwies, ist eine klinische Variante, bei welcher immer nach einem entzündlichen Prozeß gesucht werden muß, da eine Steroidtherapie hier mit Erfolg angewendet werden kann.
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Bogousslavsky, J., Perentes, E., Regli, F. et al. Polymyositis with severe facial involvement. J Neurol 228, 277–281 (1982). https://doi.org/10.1007/BF00313418
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DOI: https://doi.org/10.1007/BF00313418