Abstract
A rare combination of atrial septal defect of the secundum type and type I glycogen storage disease was seen with early fatal outcome due to rapidly progressive severe pulmonary vascular disease. Possible reasons for the unexpected, rapidly progressive pulmonary vascular disease are discussed.
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Bolz, D., Stocker, F. & Zimmermann, A. Pulmonary vascular disease in a child with atrial septal defect of the secundum type and type I glycogen storage disease. Pediatr Cardiol 17, 265–267 (1996). https://doi.org/10.1007/BF02524807
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DOI: https://doi.org/10.1007/BF02524807