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Hereditary angioedema and aortitis

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Summary

A 28-year-old male with hereditary angioedema died of an extensive stroke. Autopsy revealed cicatricial aortitis with narrowing of the coronary ostia, myocardial infarctions, and a left ventricular mural thrombus. There was neither acute inflammation of the aorta nor systemic vasculitis. A possible association of the aortitis with the hereditary angioedema is discussed.

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Abbreviations

ANA:

Antinuclear antibodies

C1-INA:

C1-inactivator

CH 50:

Total hemolytic complement

HBS-AG:

Hepatitis surface antigen

TPHA:

Treponema pallidum hemagglutination

VDRL:

Agglutination reaction for syphilis

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Authors and Affiliations

  1. Innere Medizin, Universität Heidelberg, Klinikum Mannheim

    U. Hoffmann, J. Buss & D. Heene

  2. Dermatologie, Universität Heidelberg, Klinikum Mannheim

    V. Voigtlaender

  3. Neurologie, Universität Heidelberg, Klinikum Mannheim

    P. Berlit

  4. Pathologie, Universität Heidelberg, Klinikum Mannheim

    U. Bernbeck

  5. Department of Internal Medicine Polyclinic, Angiology Division University Hospital, CH-8091, Zürich, Switzerland

    U. Hoffmann

Authors
  1. U. Hoffmann
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  2. J. Buss
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  3. V. Voigtlaender
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  4. P. Berlit
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  5. U. Bernbeck
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  6. D. Heene
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Hoffmann, U., Buss, J., Voigtlaender, V. et al. Hereditary angioedema and aortitis. Klin Wochenschr 65, 885–887 (1987). https://doi.org/10.1007/BF01737013

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  • DOI: https://doi.org/10.1007/BF01737013

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