Abstract
We report a case of Sjögren-Larsson syndrome with spastic diplegia and conduction aphasia. MRI demonstrated the white matter changes deep in the cerebral hemispheres. We analyse the MRI findings and compare the results with neuropsychological signs.
This is a preview of subscription content, log in via an institution to check access.
Similar content being viewed by others
References
Sjögren T, Larsson T (1975) Oligophrenia in combination with congenital ichthyosis and spastic disorders. Acta Psychiatr Scand 32: 1–108
Jagell S, Polland W, Sandgren O (1980) Specific changes in the fundus typical for Sjögren-Larsson syndrome: an ophthalmological study of 35 patients. Acta Ophthalmol 58: 321–330
Richards BW (1972) Sjögren-Larsson syndrome. In: Vinken PJ, Bruyn GW (eds) Handbook of clinical neurology, vol 13. North-Holland, Amsterdam, pp 468–482
Mulder LJMM, Oranje AP, Loonen MCB (1987) Cranial CT in the Sjögren-Larsson syndrome. Neuroradiology 29: 560–561
Gomori JM, Leibovici V, Zlotogorski A, Wirguin I, Haham-Zadeh S (1987) Computed tomography in Sjögren-Larsson syndrome. Neuroradiology 29: 557–559
Dubowitz LMS, Bydder GM, Mushin J (1985) Developmental sequence of periventricular leukomalacia. Arch Dis Child 60: 349–355
Koeda I, Suganuma I, Kohno Y, Takamatsu T, Takeshita K (1990) MR imaging of spastic diplegia comparative study between preterm and term infants. Neuroradiology 32: 187–190
Truwit CL, Barkovich AJ, Koch TK, Ferriero DM (1992) Cerebral palsy: MR findings in 40 patients. AJNR 13: 67–78
Benson DF, Sheremata WA, Bouchard R, Segarra JM, Proce D, Geschwind N (1973) Conduction aphasia; a clinicopathological study. Arch Neurol 28: 339–346
Sylvester PE (1969) Pathological findings in Sjögren-Larsson syndrome. Ment Defic Res 13: 267–275
Valk J, Knaap MS van der (1989) Magnetic resonance of myelin, myelination, and myelin disorders. Springer, Berlin Heidelberg New York, pp 66–94
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Hussain, M.Z., Aihara, M., Oba, H. et al. MRI of white matter changes in the Sjögren-Larsson syndrome. Neuroradiology 37, 576–577 (1995). https://doi.org/10.1007/BF00593725
Received:
Accepted:
Issue Date:
DOI: https://doi.org/10.1007/BF00593725