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Polyposis of the gallbladder associated with metachromatic leukodystrophy

  • Metabolic Diseases
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Abstract

We report on two children with metachromatic leukodystrophy and polyposis of the gallbladder. In both patients ultrasound examination revealed a small gallbladder with a thickened echogenic wall and multiple polypoid masses. In one patient diagnosis of gallbladder polyposis was made 6 months before the first neurological symptoms occurred. As gallbladder polyposis is a rare phenomenon in childhood, metachromatic leukodystrophy should be excluded.

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Authors and Affiliations

  1. Klinik mit Poliklinik für Kinder und Jugendliche der Universität Erlangen-Nürnberg, Loschgestrasse 15, W-8520, Erlangen, Germany

    M. Ries

  2. Kinderklinik Bamberg, Buger Strasse 80, W-8600, Bamberg, Germany

    K. -H. Deeg

Authors
  1. M. Ries
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  2. K. -H. Deeg
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Ries, M., Deeg, K.H. Polyposis of the gallbladder associated with metachromatic leukodystrophy. Eur J Pediatr 152, 450–451 (1993). https://doi.org/10.1007/BF01955909

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  • DOI: https://doi.org/10.1007/BF01955909

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