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Portal vein thrombosis after splenectomy for hereditary stomatocytosis in childhood

  • HEMATOLOGY/ONCOLOGY
  • Published:
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Abstract

Portal vein thrombosis is a rare but potentially lethal complication in children requiring splenectomy. We report on a 15-year-old boy with a dehydrated hereditary stomatocytosis, who underwent splenectomy and presented a postoperative partial portal vein thrombosis. With prompt heparin therapy, neither propagation of the thrombus nor further cavernous transformation in the following occurred 6 years.

Conclusion Recent data suggest that hereditary stomatocytosis carries a high risk of thrombotic complications, especially after splenectomy. This procedure, the benefit of which is limited in this condition, should therefore be strongly avoided.

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Authors and Affiliations

  1. INSERM U 409 (Institut National de la Sante et de la Recherche Scientifique), Genetique et Pathologie Moleculaires de l'Hematopoièse, Faculté de Médecine Xavier Bichat, F-75870 Paris-cedex 18, France, , , , , , FR

    D. Dhermy

  2. Service de Radiologie, Hopital des Enfants, Centre Hospitalier et Universitaire de Bordeaux, F-33076 Bordeaux-cedex, France, , , , , , FR

    J. F. Chateil

  3. Departement de Chirurgie Pédiatrique, Hopital des Enfants, Centre Hospitalier et Universitaire de Bordeaux, F-33076 Bordeaux-cedex, France, , , , , , FR

    J. M. Bondonny

  4. Laboratoire d'Hematologie, Centre Hospitalier et Universitaire de Bordeaux, F-33076 Bordeaux-cedex, France, , , , , , FR

    M. Micheau

  5. Service de Pédiatrie, Centre Hospitalier General, F-40107 Dax-cedex, France, , , , , , FR

    R. Barbier

  6. Unité d'Onco-Hematologie Pediatrique, Hopital des Enfants, Centre Hospitalier et Universitaire de Bordeaux, Place Amelie Raba-Leon, F-33076 Bordeaux-cedex, France e-mail: yves.perel@chu-aquitaine.fr, Tel.: +33-5-56-79-56-41, Fax: +33-5-56-79-60-54, , , , , , FR

    Y. Perel & A. Carrere

Authors
  1. Y. Perel
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  2. D. Dhermy
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  3. A. Carrere
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  4. J. F. Chateil
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  5. J. M. Bondonny
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  6. M. Micheau
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  7. R. Barbier
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Additional information

Received: 28 May 1998 / Accepted in revised form: 6 October 1998

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Perel, Y., Dhermy, D., Carrere, A. et al. Portal vein thrombosis after splenectomy for hereditary stomatocytosis in childhood. Eur J Pediatr 158, 628–630 (1999). https://doi.org/10.1007/s004310051165

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  • DOI: https://doi.org/10.1007/s004310051165

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