Summary
Vacuoles could be demonstrated in nearly all plasma cells and in some lymphocytes of an adult with glycogenosis type II-acid maltase deficiency. Electronmicroscopical, microspektrophotometrical, and cytochemical investigations revealed glycoproteid inclusions.
Zusammenfassung
Bei Glykogenose II — Sauerer Maltasemangel — wurden bei einem erwachsenen Patienten regelmäßig Vacuolen in Plasmazellen und vereinzelt in Lymphocyten gefunden, die nach elektronenmikroskopischen, mikrospektrophotometrischen und cytochemischen Untersuchungen Glykoproteideinschlüssen entsprechen.
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Literatur
Angelini, C., Engel, A. G.: Comparative study of acid maltase deficiency. Biochemical differences between infantile, childhood and adult types. Arch. Neurol. (Chic.)26, 344–349 (1972).
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Pralle, H., Schroeder, R. & Löffler, H. Plasmazelleinschlüsse bei Mangel an saurer Maltase (Glycogenose Typ II). Klin Wochenschr 52, 653–654 (1974). https://doi.org/10.1007/BF01468804
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DOI: https://doi.org/10.1007/BF01468804
Key words
- Glycogenosis type II-acid maltase deficiency
- plasma cells
- lymphocytes
- inclusion bodies
- electron microscopy
- microspectrophotometry
- cytochemistry