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Profound muscle weakness associated with axis cylinder ballooning

A case report

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Summary

Multifocal central white matter axonal swelling characterized electron microscopically by focal axonal mitochondrial and membraneous body enrichment occurred in a 52 year old man who presented with the chief complaint of severe progressive muscular weakness accompanied by disorientation. The clinical and pathological findings in this patient appear unique and are presented in order to broaden our concepts of axis cylinder pathology.

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Authors and Affiliations

  1. Department of Pathology at Veterans Administration Hospital, 11768, Northport, New York, USA

    Nancy S. Peress & Byung-Hoon Kim

  2. Department of Pathology at State University of New York, Stony Brook, New York

    Nancy S. Peress & Byung-Hoon Kim

  3. Department of Pathology at Downstate Medical Center, New York, New York

    Nancy S. Peress & Byung-Hoon Kim

Authors
  1. Nancy S. Peress
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  2. Byung-Hoon Kim
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Peress, N.S., Kim, BH. Profound muscle weakness associated with axis cylinder ballooning. Acta Neuropathol 28, 87–92 (1974). https://doi.org/10.1007/BF00687522

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  • DOI: https://doi.org/10.1007/BF00687522

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