Summary
Abnormal Schwann cell inclusion is reported in biopsied peripheral nerve in a cases of infantile neuroaxonal dystrophy.
In addition to non-specific dystrophic changes of the axons, the Schwann cells contained several distinct bodies which were composed of stacks of irregularly disposed membranes; in some instances, transformed Schwann cell cytoplasm was distinded with similar bodies. This change has not been reported on this condition and its significance is briefly discussed.
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References
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Yagishita, S., Itoh, Y., Nakano, T. et al. Infantile neuroaxonal dystrophy. Acta Neuropathol 41, 257–259 (1978). https://doi.org/10.1007/BF00690446
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DOI: https://doi.org/10.1007/BF00690446