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Peripheral medulloepithelioma

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Summary

A case of congenital peripheral medullo-epithelioma arising in the sciatic nerve of a 6-month-old boy is reported. Histologically, areas of primitive neural tumor merged with areas showing differentiation into ependymoma, astrocytoma, oligodendroglioma, and ganglioneuroma. These lines of differentiation were confirmed by electron microscopy and immunohistochemistry. Despite the malignant nature of the tumor, 7 years after amputation of the affected leg, the child is alive without recurrence.

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Nakamura, Y., Becker, L.E., Mancer, K. et al. Peripheral medulloepithelioma. Acta Neuropathol 57, 137–142 (1982). https://doi.org/10.1007/BF00685381

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  • DOI: https://doi.org/10.1007/BF00685381

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