Abstract
The activities of the last twenty years of the Iowa clinic for neuromuscular diseases are briefly reviewed. Main emphasis in this paper is on management and guidance of the patient with Duchenne muscular dystrophy (DMD) by the families, the school and the public at large. Guidance and treatment given to our patients is briefly described. It is well known that chronic debilitating disease affects not only the patient but the whole family; management of DMD should therefore include the parents and siblings of the patient. Preventability of DMD is illustrated by the experiences in our clinic. The importance of early carrier detection and genetic counseling is stressed. Possible future developments in DMD research are briefly mentioned.
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Herrn Prof. Dr. H.-R. Wiedemann, gewidmet zu seinem 65. Geburtstag
Curriculum vitae. Hans Zellweger, born in Lugano, Switzerland, graduated from the University of Zürich in 1934. After three years at the Kantonspital in Lucerne (Pathology, Microbiology) and two years with Dr. Albert Schweitzer in Lambarene he spent twelve years with Prof. G. Fanconi in the Kinderspital Zurich. He was general secretary of the International Congress of Pediatrics in Zurich, 1950. From 1951 to 1959 he was chairman of the Pediatrics Department of the American University in Beirut, Lebanon. Since 1959 he is Professor of Pediatrics at the University of Iowa, Iowa City, Iowa. He opened one of the first laboratories for cytogenetics in 1960. Thereafter he became director of the Genetic Clinic and founded a clinic for neuromuscular disease. In 1976 he organized with Jane Simpson the Regional Genetic Consultation Service for the whole State of Iowa, with fifteen genetic counseling clinics through the State of Iowa. He became Professor Emeritus in 1977, yet is still active in the genetic clinic. Dr. Victor Ionasescu is Director of the Clinic for Neuromuscular Diseases and Chief of the Laboratory for Muscle Research at the University of Iowa, Department of Pediatrics.
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Zellweger, H., Simpson, J. & Ionasescu, V. Twenty years-iowa muscle clinic: Reminiscences and prospects. Eur J Pediatr 138, 17–22 (1982). https://doi.org/10.1007/BF00442321
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DOI: https://doi.org/10.1007/BF00442321