Abstract
The daily Phe intakes of normally growing 1- to 6-year-old treated PKU patients were evaluated. The children received protein in amounts that varied from 2.26±0.47 g/kg body weight per day (mean±SD) at the age of 6 to 1.81±0.35 at the age of 72 months. Mean Phe intakes declining from 34±7 at the age of 6 months to 15±5 mg/kg body weight per day at the age of 72 months were required to maintain mean median plasma Phe levels around 6.0 mg/dl.
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Wendel, U., Ullrich, K., Schmidt, H. et al. Six-year follow up of phenylalanine intakes and plasma phenylalanine concentrations. Eur J Pediatr 149 (Suppl 1), 13–16 (1990). https://doi.org/10.1007/BF02126293
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DOI: https://doi.org/10.1007/BF02126293