ISSN:
1432-0533
Keywords:
Primary familial amyloidosis
;
Vitreous opacities
;
Meningovascular deposition
;
Extensive cerebral infarction
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Summary A 41-year-old Japanese male with a new type of primary familial amyloidosis was reported. The patient developed vitreous opacities, and later, disturbances in the gastrointestinal and nervous systems. At autopsy, amyloid was observed in the vitreous and the retinal vessels. There were extensive cerebral infarcts and heavy meningo-vascular amyloid deposition. Although the postmortem study revealed slight peripheral nerve degeneration in the lower extremities secondary to amyloid deposition, there was no clinical evidence of polyneuropathy.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF01273271