ISSN:
1530-0358
Keywords:
Familial adenomatous polyposis
;
Desmoid
;
Intrahepatic
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Abstract Desmoids are uncommon proliferations of fibroblasts that occur with disproportionate frequency in patients with familial adenomatous polyposis. They do not metastasize and are histologically benign. Despite this, the unpredictable and often aggressive nature of familial adenomatous polyposis-associated desmoids and their tendency to occur in intra-abdominal sites means that they present a difficult management problem, and they are a leading cause of death in patients with familial adenomatous polyposis who have undergone colectomy. We report a case of a patient with familial adenomatous polyposis who had extensive and aggressive desmoid disease and whose management was further complicated by a large intrahepatic desmoid. There are no previous reports of desmoids occurring in the liver.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF02237369
