ISSN:
1432-1076
Keywords:
Glycogen storage disease type I
;
Hypoglycemia
;
Hypertriglyceridemia
;
Growth rate
;
α-Glucosidase inhibitor
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Abstract Seven patients with glycogen disease type I have been treated with nocturnal intragastric feeding combined with frequent daytime feeding. Follow-up shows a striking improvement in their clinical condition including growth rate. Determination of biochemical parameters reveals a significant increase of lactate, pyruvate, alanine, uric acid, triglycerides, and SGOT in blood. Additional administration of an α-glucosidase inhibitor in four patients caused a significant increase in blood lactate despite unchanged blood glucose levels.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF00441652