ISSN:
1432-1076
Keywords:
Lysinuric protein intolerance
;
Growth hormone
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Abstract Our two patients with lysinuric protein intolerance, a 14-year-old boy and his 12-year-old sister, showed growth retardation and their bone ages were retarded. Growth hormone secretion responded to glucagon-propranolol and showed a good response to arginine. However, growth hormone showed little response to insulin. After the oral administration of arginine hydrochloride, growth hormone showed a good response to insulin and glucagon-propranolol, and gain in height and weight accelerated. This result may suggest that an adequate supply of arginine is effective in improving the growth retardation in lysinuric protein intolerance.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF00572769