ISSN:
1437-9813
Keywords:
Hirschsprung's disease
;
Total colonic aganglionosis
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Abstract Thirty-two patients with total colonic aganglionosis (TCA) were seen in 30 years, representing 10% of the total number with aganglionosis seen during that period (1954–1983). The mortality rate was 45%, but has shown a progressive decrease from 82% in the first decade to 9% in the last. The improvement is specifically related to earlier diagnosis, control of sepsis, and the use of parenteral nutrition in dealing with ileostomy losses, but appears to have been independent of the definitive surgical procedure. Follow-up study indicates some delay in achieving continence without any clear-cut relationship to the operative procedure. The 32 patients have been reviewed with particular emphasis on sex ratio, age at diagnosis, clinical features, and results of treatment.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF00174176
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