ISSN:
1432-1920
Keywords:
Key words Hunter's syndrome
;
Mucopolysaccharidosis
;
Magnetic resonance imaging
;
Computed tomography
;
Virchow-Robin spaces
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Abstract We report imaging findings in a 3-year-old boy with the typical mild type of Hunter's disease. MRI revealed multifocal large cyst- or spindle-like areas of increased and decreased signal in the white matter, including the corpus callosum on T1- and T2-weighted images. The white matter showed high signal on T2-weighted images, isointense with cerebrospinal fluid on all other pulse sequences. To our knowledge, these appearances have not been reported in this disorder. Deposition of mucopolysaccharide and/or glycolipid and increase in fluid content seem to be responsible.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF00607284
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