ISSN:
1432-1084
Keywords:
Bone, sclerosis
;
Erdheim-Chester disease
;
High-resolution computed tomography (HRCT)
;
Interstitial lung disease
;
Lipogranulomatosis
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Abstract Erdheim-Chester disease is a distinctive pathological radiographic entity, most commonly characterised by a typical skeletal involvement resulting from histiocytic infiltration of the bone marrow. Although lung involvement is often absent, we report a case of diffuse infiltrative lung disease characterised by a wide-spread reticular pattern on high-resolution CT scans associated with cystic airspaces and mild honeycombing observed throughout both lungs. Interstitial infiltration with lipid-laden histiocytes was histologically confirmed by means of transbronchial biopsy.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF00167478
