ISSN:
1432-0533
Keywords:
Pallido-nigro-luysial atrophy
;
Combined system degeneration
;
Progressive supranuclear palsy
;
Corpora amylacea
Source:
Springer Online Journal Archives 1860-2000
Topics:
Medicine
Notes:
Summary A case of pallido-nigro-luysial atrophy, characterized by symptoms typical of progressive supranuclear palsy, presented (1) severe symmetrical abiotrophic degeneration of the globus pallidus, substantia nigra, and subthalamic nucleus and (2) widespread accumulations of corpora amylacea in the CNS. The former is thought to be consistent with pallidonigro-luysial atrophy and we regard it as a combined system degeneration of both the pallido-nigral and the pallido-luysial systems. The significance of the latter is quite obscure. As far as we know, only three cases of pallido-nigro-luysial atrophy have been reported. However, there is no reported case of this disorder with such widespread and massive accumulations of corpora amylacea as in our case.
Type of Medium:
Electronic Resource
URL:
http://dx.doi.org/10.1007/BF00689999
